ABSTRACT
El Fibroma Desmoplástico es una patología poco frecuente y de localización mas conocida en maxilar inferior y pocos casos en tibia, fémur y otros huesos. En rótula no se encontraron casos en la abundante bibliografía consultada. Se presenta un caso en un paciente de 15 años que después de un año de tratamiento médico y fisiokinésico se hace RMN y TAC encontrando una imágen osteolítica en rótula izquierda, por lo que después de interconsulta con Ortopedista y Traumatólogo Infantil, se resuelve tratamiento quirúrgico. El objetivo de esta presentación es llamar la atención sobre dolor que se interpreta como tendinitis cuadricipital, con Rx. neg. y dolor en borde proximal de rótula y borde externo de la misma, pero los estudios mencionados nos orientan a una patología muy poco frecuente. Además se destaca que no se encontró en la bibliografía antecedente de otro caso similar en rótula. Se hace resección con margen de seguridad de la zona afectada incluyendo hueso y cartílago articular. La evolución fue satisfactoria, controlado a los 3 años no hay dolor ni limitación funcional. Tipo de estudio: Reporte de caso. Nivel de evidencia: IV
The Desmoplastic Fibroma is an unfrequent pathology and the most common location is in the lower jaw (there are a few cases in the tibia, femur and other bones). There wasn't found a case in the kneecap, despite the extensive bibliography consulted. It is presented a case of a 15 years old patient who after a year of medical and physio-kinesic treatment, underwent MRI and CT scans, finding an osteolytic image in the left patella. After consulting with an Orthopedist and a Child Traumatologist, it was resolved a surgical treatment. The purpose of this presentation is to draw attention to a pain in the proximal and outer edges of the patella interpreted as quadriceps tendonitis, without seeing anything in a radiography. It was made a resection, with a safety margin of the affected area, including bone and articular cartilage. There was a satisfying evolution, checked after 3 years, without pain or functional limitation. Type of Study: case report. Level of evidence: IV
Subject(s)
Adolescent , Patella/pathology , Fibroma, Desmoplastic/surgery , Fibroma, Desmoplastic/diagnosis , Knee Joint/surgery , Treatment OutcomeABSTRACT
El fibroma desmóplasico es una neoplasia benigna del tejido conjuntivo que tiene alta capacidad de infiltrar los tejidos adyacentes. En este artículo se presenta un caso clínico de una paciente de 3 a±os de edad con un fibroma desmoplßsico en la región sinfisiaria y en el cuerpo mandibular. El tratamiento fue la hemimandibulectomía y la colocación de injerto óseo autólogo y placa de reconstrucción. Se realizó una revisión de la literatura de este tumor benigno poco frecuente de la región maxilo facial...
Desmoplasic fibroma is a benign connective tissue tumor with high local infiltration capacity. This article presents a case of a 3-yearoldgirl who presented a desmoplasic fibroma in the mandible symphysis and body. The treatment was radical resection and placement of an autologous bone graft and reconstruction plate. A review of the published literature was done respect to this rare benign tumor of the maxillofacial region...
Subject(s)
Humans , Female , Child, Preschool , Fibroma, Desmoplastic/surgery , Fibroma, Desmoplastic/diagnosis , Fibroma, Desmoplastic/pathology , Fibroma, Desmoplastic , Mandibular Neoplasms/diagnosis , Diagnostic Imaging , Tomography, X-Ray Computed , Bone TransplantationABSTRACT
Desmoplastic fibroma of bone is a rare locally aggressive, but non-metastatic tumor. In this case report, we present a desmoplastic fibroma in an unusual location, the clavicle. Desmoplastic fibroma involving the clavicle is extremely rare, with only 2 reported cases before 1985. We report the imaging findings of a desmoplastic fibroma of the clavicle with a review of the relevant literature.
Subject(s)
Adult , Humans , Male , Bone Neoplasms/diagnosis , Clavicle/pathology , Fibroma, Desmoplastic/diagnosis , Magnetic Resonance Imaging , Tomography, X-Ray ComputedABSTRACT
Extra-abdominal fibromatosis is a benign fibrous neoplasm of locally aggressive behavior. Surgical excision with a wide margin is the treatment of choice. The aim of the present work is to report the case of fibromatosis in an 11-year-old melanodermic patient, who showed swelling in the area of the right mandible. Conservative surgery was performed based on the initial histopathological diagnosis of benign lesion suggestive of neural origin. The new anatomopathological examination of the surgical specimen was compatible with fibromatosis. The patient is still under periodic observation as part of the five-year surgical follow-up, showing no signs of recurrence.
Fibromatose extra-abdominal é uma neoplasia fibrosa benigna, caracterizada por comportamento agressivo local. Geralmente, o tratamento de escolha consiste na excisão cirúrgica com ampla margem de segurança. O objetivo deste trabalho é relatar um caso de fibromatose em uma paciente de 11 anos, melanoderma, que apresenta aumento de volume na mandíbula do lado direito. A partir do diagnóstico histopatológico inicial sugestivo de lesão benigna de origem neural, foi realizado tratamento cirúrgico conservador. Um novo exame anatomopatológico da peça cirúrgica foi compatível com fibromatose. A paciente encontra-se sob controle periódico de cinco anos da cirurgia, não havendo recorrência clínica da lesão.
Subject(s)
Humans , Female , Child , Fibroma, Desmoplastic/surgery , Fibroma, Desmoplastic/diagnosis , Fibromatosis, Abdominal/diagnosis , Fibromatosis, Aggressive/diagnosis , Mandible/pathologyABSTRACT
Desmoplastic fibroma is a rare benign primary bone tumor that is histologically similar to the soft tissue desmoid tumor. It most often involves the mandible, large long bone or iliac bone. Desmoplastic fibroma in a toe has been extremely rarely reported. Authors report a rare case of desmoplastic fibroma of bone occurring in the distal phalanx of a foot, with descriptions of the radiographic and MRI findings, correlation of the radiologic and pathologic findings, and discussion on the differential diagnosis of the tumor.
Subject(s)
Adolescent , Female , Humans , Male , Bone Neoplasms/diagnosis , Diagnosis, Differential , Fibroma, Desmoplastic/diagnosis , Magnetic Resonance Imaging , Toes/pathologyABSTRACT
Infantile desmoplastic fibromatoses are benign fibrous tissue tumours, non -metastasizing but locally aggressive and with high likelihood of recurrence. Many cases occur in young children between 18 months and 3 years and commonly present as painless mass of the submandibular region. The maxilla is rarely involved. Through this report and a review of literature, we are going to study clinical, pathological and prognostic characteristics of this affection. We report here a case of an aggressive desmoplastic fibroma arising in a 20-months-old infant originating in the left anterior maxillary wall. Clinical examination of the face revealed a non tender, firm, expansion of the left maxilla of 2.5 cm of diameter. The diagnosis of DF of the maxilla was made on the basis of histological features on biopsy specimen. No other location of the fibromatosis was found. The child had a favourable course. DF is an intraosseous, non metastasizing and locally aggressive fibrous tumour. Although its benignity it could engage vital prognosis since it can extend into vital organs